Hemophagocytic Lymphohistiocytosis in a Patient with Adult-Onset Still’s Disease – a Diagnostic Dilemma
| International Journal of Medical Science |
| © 2017 by SSRG - IJMS Journal |
| Volume 4 Issue 4 |
| Year of Publication : 2017 |
| Authors : Priyank Gupta, Roopesh Pandey and Chetan Unadkat |
10.14445/23939117/IJMS-V4I4P103
How to Cite?
Priyank Gupta, Roopesh Pandey and Chetan Unadkat, "Hemophagocytic Lymphohistiocytosis in a Patient with Adult-Onset Still’s Disease – a Diagnostic Dilemma," SSRG International Journal of Medical Science, vol. 4, no. 4, pp. 8-10, 2017. Crossref, https://doi.org/10.14445/23939117/IJMS-V4I4P103
Abstract:
Hemophagocytic lymphohistiocytosis (HLH) is a serious complication of Adult-onset Still’s Disease(AOSD) and because of their overlapping clinical features, there will be delay in the diagnosis leading to increased morbidity and mortality. Here we present a case report of 61 years old female patient who were diagnosed with AOSD associated with secondary HLH, which despite treatment, led to fatal outcome.
Keywords:
Hemophagocytic lymphohistiocytosis, Adult-onset Still’s Disease, Ferritin.
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